Journal of Disability and Oral Health

cover art

Cover Date:
September 2017
Print ISSN:
1470-8558
Vol:
18
Issue:
3

Fibrodysplasia ossificans progressiva and its implications for dental treatment (FOP): A case report

Aims: This case report discusses the general and dental manifestations of fibrodysplasia ossificans progressiva
(FOP) and details the dental management considerations particular to this case. Methods: A case report methodology was employed to describe the clinical encounter of a patient with FOP. Case summary: FOP is an extremely rare hereditary disorder characterised by progressive ossification of the tendons, ligaments, fasciae and striated muscles. The patient’s primary oral complaint was a complete inability to separate the upper and lower jaws, which were “locked” into position. At the age of twenty he underwent extraction of the lower right third molar, which led to progressive ossification and subsequent fixation of the jaws. The patient presented with pain and dental infection over multiple appointments. Treatment planning involved a multi-professional approach including oral and maxillofacial surgery, oral surgery and special care dentistry teams. A novel approach using cone beam computed tomography to identify the location and extent of carious lesions was used. Risk assessment was critical as dental extractions posed a risk of uncontrolled heterotrophic bone formation; the provision of dental restorations posed the risk of inadequate visualisation / placement and trauma to the oral tissues when retracting. Conclusions: This case poses both a clinical and ethical dilemma. After weighing the potential risks and benefits of dental treatment, there was no clear answer to this case – the plan is for the multi-disciplinary team to provide high quality preventative care and monitor the patient closely, with surgical intervention dictated by pain / infection
frequency and any further dental deterioration.

Key words: Special care dentistry, fibrodysplasia ossificans progressiva

Article Price
£15.00
Institution Article Price
£
Page Start
101
Page End
105
Authors
J Doughty, C Steel, P Thakrar, N Kumar

Articles from this issue

  • Title
  • Pg. Start
  • Pg. End

  1. Editorial
  2. 74
  3. 75

  1. iADH Invitation
  2. 76
  3. 76

  1. Conscious sedation using propofol for the treatment of patients with hypersensitive gag reflexes
  2. 77
  3. 86

  1. Patient referrals to special needs dental units in Tasmania, Australia
  2. 87
  3. 94

  1. The oral health status of Special Olympics athletes in Trinidad and Tobago: thirteen years later
  2. 95
  3. 100

  1. Fibrodysplasia ossificans progressiva and its implications for dental treatment (FOP): A case report
  2. 101
  3. 105

  1. Continuing Professional Development Programme
  2. 106
  3. 107

  1. Diary Dates 2017-2018
  2. 108
  3. 108

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